1Department of Pedodontics & Preventive Dentistry, Rajah Muthiah Dental College & Hospital, Annamalai University, Chidambaram, Tamilnadu.
2Department of Pedodontics & Preventive Dentistry, Govt Dental College, Chattisgarh.
3Priyadarshini Dental College, Thiruvallur Dist. Tamilnadu.
Ectodermal dysplasia is a rare hereditary disorder. Its Hypohidrotic (HED) variant is also known as Christ-Siemens-Touraine syndrome. It is inherited as an X- linked trait. Such patients are characterized by the clinical manifestations of Hypodontia, Hypotrichosis, Hypohidrosis and a highly characteristic facial physiognomy. This article reports a typical case of Hypohidrotic Ectodermal Dysplasia (HED) and its management.
Ectodermal dysplasia, Hypohidrotic ectodermal dysplasia, Hypodontia, Hypotrichosis, Hypohidrosis
