Genetic disorders account for a significant amount of morbidity and mortality in children and are of primary interest to the dentist. Crouzan syndrome is one of a rare group of syndromes characterized by craniosynostosis or premature closing of the cranial sutures. The major features are Brachycephaly, ocular proptosis, under developed maxilla, midface hypoplasia, rare cleft lip, palate. Early Craniectomy is often needed to alleviate the raised intracranial pressure. This paper discusses a case report of five year old girl with the features of crouzan syndrome and a multidisciplinary approach to be followed in managing the situation.
Craniofacial syndromes, Crouzon, Premature Synostosis
