Annals and Essences of Dentistry

  • Year: 2011
  • Volume: 3
  • Issue: 2

Papillion lefevre syndrome -a case report

  • Author:
  • Padmavathi K1,, Hari Devaraya Chowdary2
  • Total Page Count: 3
  • DOI:
  • Page Number: 66 to 68

1Department of periodontics, Rungta Dental College, Bhillai, Chattisgarh

2Department of Community Dentistry, Rungta Dental College, Bhillai, Chattisgarh

Corresponding Author: Dr. padmavathy K, Professor, Department of periodontics, Rungta Dental College, Bhillai, Chattisgarh. Email: hyd_dentist@yahoo.com Ph:+ 919440376777

Online published on 22 September, 2011.

Abstract

Papillion Lefevre syndrome (PLS) is a rare disease associated with skin lesions, severe destruction of periodontium and in some cases, calcification of dura. Skin lesions consist of hyperkeratosis and icthyosis of localized areas on palms, soles, knees and elbows, multiple functional neutrophil defects, including myeloperoxidase deficiency as well as defective chemotaxis and phagocytosis.

Keywords

Papillion Lefevre syndrome (PLS), Hyperkeratosis, Neutrophil, periodontitis, phagocytosis