1Department of Oral and Maxillofacial Surgery, Punjab Government Dental College and Hospital, Amritsar, Punjab, India
2Department of Oral and Maxillofacial Surgery, Punjab Government Dental College and Hospital, Amritsar, Punjab, India
3Department of Oral and Maxillofacial Surgery, Punjab Government Dental College and Hospital, Amritsar, Punjab, India
*Corresponding Author: Dr. Neetu Pansotra, Department of Oral and Maxillofacial Surgery, Punjab Government Dental College and Hospital, Amritsar, Punjab, India. E-mail: neetupansotra@gmail.com
Online published on 17 November, 2021.
The Gorlin-Goltz syndrome (GGS), also known as Nevoid basal cell carcinoma syndrome(NBCCS) is a rare hereditary autosomal-dominant disorder characterised by multiple odontogenic keratocysts, basal cell carcinomas of skin as well as various neurological, ocular, skeletal, genitourinary disorders. Diagnosis of the syndrome is based on major and minor criterias first given by Evans et al (1993) which was later modified by kimonis et al (1997). Very few cases of this syndrome have been reported with familial background from India. We present a rare case report of Gorlin-Goltz syndrome with familial pattern affecting son and his mother.
Gorlin–goltz syndrome, Nevoid Basal Cell Carcinoma Syndrome, Odontogenic Keratocysts, Mandible, Maxilla
