Online published on 28 May, 2014.
Odontogenic keratocysts (OKCs) are epithelial developmental cysts which were first described by Phillipsen in 1956. Lesions are frequently multiple and by with a component of Nevoid Basal Cell Carcinoma Syndrome (NBCCS). We hereby report a case of multiple OKCs in a non syndromic patient and highlight the general practitioner the importance of diagnosing the disease and enforcing a strict long-term follow-up whenever such a case is identified.