Indian Journal of Contemporary Dentistry
  • Year: 2016
  • Volume: 4
  • Issue: 2

Unusual Appearances of Cleidocranial Dysplasia: A Case Report

  • Author:
  • Puneet Bhargava1, Rohit Sharma1, Mayank Das2, Chandni Shekawat3, Saba Khan4, Akshay Verma5,, Ajay Sharma5
  • Total Page Count: 4
  • Page Number: 26 to 29

1Associate Professor, Department of Oral Medicine, Radiology and Diagnosis, NIMS Dental College & Hospital, Jaipur, India

2Assistant Professor, Department of Oral Medicine, Radiology and Diagnosis, NIMS Dental College & Hospital, Jaipur, India

3Assistant Professor, Department of Oral Medicine, Radiology and Diagnosis, Government Dental College & Hospital, Jaipur, India

4Assistant Professor, Department of Oral Medicine, Radiology and Diagnosis, Darshan Dental College & Hospital, Udaipur, India

5Assistant Professor, Department of Oral Pathology and Microbiology, Rajasthan Dental College and Hospital, Jaipur

*Corresponding author: Dr. Akshay Verma, Seniour Lecturer, Department of Oral Pathology and microbiology, Rajasthan Dental College & Hospital, Jaipur, Rajasthan, India. E-mail: dr.akashyavermaop@gmail.com, Ph no.-+91-9509222226

Online published on 20 August, 2016.

Abstract

Cleidocranial Dysplasia is a rare autosomal dominant disorder affecting skull, jaws, teeth, clavicle along with other skeletal abnormalities. Its prevalence is estimated at 1 per 1 million. This condition may be inherited, be transmitted as dominant characteristics in either sex, or even may appear spontaneously. It presents with skeletal defects of several bones, like partial or complete absence of clavicles, late closure of the fontanels, presence of open skull sutures and multiple wormian bones. Case like this concerns the Dental surgeon as it shows multiple numbers of impacted and supernumerary teeth.

Keywords

Clavicle, Cleidocranial Dysplasia, Hypoplasia of masseter muscle, Impacted teeth, Supernumerary Teeth