Indian Journal of Clinical and Experimental Dermatology
  • Year: 2018
  • Volume: 4
  • Issue: 3

Generalized Dowling Degos disease: A rare genetic disorder

1Professor, Dept. of Dermatology, Sri Guru Ram Das Institute Of Medical Sciences and Research, Amritsar, Punjab, India

2Junior Resident, Dept. of Dermatology, Sri Guru Ram Das Institute Of Medical Sciences and Research, Amritsar, Punjab, India

3Professor, Dept. of Physiology, Sri Guru Ram Das Institute Of Medical Sciences and Research, Amritsar, Punjab, India

*Corresponding Author: Email: drsaurabhsharma@yahoo.co.in

Online published on 14 January, 2019.

Abstract

Dowling Degos disease (DDD) is an uncommon, autosomal dominant genodermatosis characterized by acquired, flexural hyperpigmentation. Clinico-histopathological correlation is diagnostic showing multiple hyperpigmented macules clinically and marked, heavily pigmented, slender and elongated rete ridges on histology. This entity needs to be differentiated from other reticulate hyperpigmentary disorders. Due to rarity of this condition, we report a case of generalized Dowling Degos disease in an adolescent female.

Keywords

Dowling Degos disease, Genodermatosis, Hyperpigmentation