Indian Journal of Mednodent and Allied Sciences
Open Access
  • Year: 2014
  • Volume: 2
  • Issue: 1

Clouston's Syndrome—A Case Report

Department of Dermatology, Shanthiram Medical College and Hospital, Nandyal, Andhra Pradesh, India

*Corresponding Author Email: vc.madhavi@gmail.com

Online published on 15 May, 2014.

Abstract

Clouston's syndrome or Hidrotic ectodermal dysplasia is an autosomal-dominant inherited rare ectodermal dysplastic disorder characterized by triad of nail dystrophy, palmoplantar keratoderma, and alopecia. Here we present a case report of clouston syndrome with classical triad along with hypodontia, microdontia and severe mental retardation. This is being reported because of it is rarity.

Keywords

Alopecia, Clouston's syndrome, Hidrotic ectodermal dysplasia, Nail dystrophy, Palmoplantar keratoderma