Indian Journal of Mednodent and Allied Sciences
Open Access
  • Year: 2014
  • Volume: 2
  • Issue: 2

Pachyonychia Congenita Type II: A Case Report

Department of Dermatology, Santhiram Medical College and Hospital, Nandyal, Andhra Pradesh, India

*Corresponding author email id: vc.madhavi@gmail.com

Online published on 11 November, 2014.

Abstract

Pachyonychia congenita type II is an autosomal dominant inherited rare genodermatosis characterized by dystrophic wedge shaped thickened nails with subungual hyperkeratosis, symmetric palmoplantar keratoderma, steatocystoma multiplex. Here we report a 23-year-old male with characteristic features of dystrophic nails, palmoplantar keratoderma, steatocystoma multiplex, follicular hyperkeratotic papules and history of natal teeth at birth.

Keywords

Dystrophic nails, Palmoplantar keratoderma, Natal teeth, Steatocystoma multiplex