Indian Journal of Mednodent and Allied Sciences
Open Access
  • Year: 2017
  • Volume: 5
  • Issue: 3

Papillon-Lefevre Syndrome-A Report of Two Cases

1Associate Professor, Deptartment of Oral and Maxillofacial Surgery, GDC & H, RIMS, Kadapa, Andhra Pradesh, India

2Post Graduate, Department of Oral Medicine and Radiology, GDC & H, RIMS, Kadapa, Andhra Pradesh, India

3Assistant Professor, Department of Oral Medicine and Radiology, GDC & H, RIMS, Kadapa, Andhra Pradesh, India. sindhudentalsdnr@gmail.com

4Post Graduate, Department of Oral Medicine and Radiology, GDC & H, RIMS, Kadapa, Andhra Pradesh, India. juwerias1@gmail.com

*Corresponding author email id: sindhudentalsdnr@gmail.com

Online published on 14 March, 2018.

Abstract

Papillon-Lefevre syndrome is a rare autosomal recessive trait characterised by palmoplantar hyperkeratosis and precocious loss of both deciduous and permanent teeth. The aetiology is multifactorial with genetic, immunological, microbiological factors being considered a main etiopathogenic factors. We present here two cases of two siblings affected with Papillon-Lefevre syndrome.

Keywords

Papillon-Lefevre syndrome, Palmoplantar hyperkeratosis, Precocious loss of teeth