Congenital High Airway Obstruction Syndrome (CHAOS)

This is a case report of preterm male child weighing 1.9 Kg, APGAR 2/10-3/10 with tracheal stenosis, web or agenesis. Mother was taking phenytoin and on ANC showing oligohydramnios. It was done in 2nd trimester showing age 21 weeks 2 days with congenital high airway obstruction syndrome with enlarged hypoechoic lungs, compressed tubular heart and massive ascitis. This syndrome is associated with a poor prognosis. Baby was delivered via NVD with signs suggestive of fetal hydrops. Inspite of best efforts baby could not be saved.