International Journal of Medical Research & Health Sciences
  • Year: 2015
  • Volume: 4
  • Issue: 3

Prosthetic management of patient with papillon-lefevre syndrome: a clinical report

  • Author:
  • Sushen Sharma1,, Akhil Mittal1, TK Gir2, Bhaskar Sengupta3, Vishal Jain4
  • Total Page Count: 5
  • Page Number: 708 to 712

1PG student, Department of Prosthodontics, DR R Ahmed Dental College & Hospital, Kolkata, India

2Professor, DR R Ahmed Dental College & Hospital, Kolkata, India

3Professor & HOD, Department of Prosthodontics, Principal, DR R Ahmed Dental College & Hospital, Kolkata, India

4PG student, Department of Paedodontics & Preventive Dentistry, DR R Ahmed Dental College & Hospital, Kolkata, India

*Corresponding author email: akhilmitta1l988@gmail.com

Online published on 29 July, 2015.

Abstract

Papilion Lefevre syndrome is a rare autosomal recessive genetic disorder, which is characterized by palmarplantar hyperkeratosis, with rapidly progressive periodontitis and premature loss of both deciduous and permanent teeth. The etiology of PLS is multifactorial with genetic, immunological, and microbial factors playing a role in etiopathogenesis. This is a case report of prosthodontic rehabilitation of a 14-year-old boy with Papillon-Lefevre syndrome.

Keywords

Papillon Lefevre syndrome, Palmoplantar hyperkeratosis, Periodontitis, Overlay prosthesis