1Assistant Professor of Neurology Shahid Beheshti University of Medical Science Loghman Hakim Hospital, Iran
2MD Rheumatology Fellowship Iran University of Medical Science (IUMS) Hazrat Rasool General Hospital, Iran
3Associate Professor of Infectious Disease Shahid Beheshti University of Medical Science Loghman Hakim Hospital, Iran
4MD Neurology Resident Shahid Beheshti University of Medical Science Loghman Hakim Hospital, Iran
*Corresponding email: dr.navid57@gmail.com
Online published on 29 September, 2018.
We report the treatment and follow-up, including magnetic resonance imaging (MRI) of a patient with idiopathic hypertrophic pachymeningitis and review the literature published in 21th century, with emphasis on the management and clinical outcomes of this rare disorder. Hypertrophic pachymeningitis is extremely rare. It is a fibrosing inflammatory process which involves the dura mater. Numerous pathological entities produce thickening of the pachymeninges. Thus, idiopathic hypertrophic pachymeningitis is diagnosed by exclusion. We present a case of patient with idiopathic hypertrophic pachymeningitis who had varied clinical presentation. Imaging studies revealed diffuse thickening of the pachymeninges.
Pachymeningitis, Hypertrophic, Review
