International Journal of Medical Research & Health Sciences
  • Year: 2017
  • Volume: 6
  • Issue: 7

Sickle Beta Plus Thalassemia Presenting as Acute Pancreatitis-A Case Report

  • Author:
  • Lalit Mohan Bhardwaj1,, PC Bhattacharyya2, Swapnav Borthakur3
  • Total Page Count: 2
  • Page Number: 40 to 41

1DNB PGT, General Medicine, Department of Medicine, Downtown Hospital, Guwahati, Assam, India

2Senior Consultant, Department of Medicine, Downtown Hospital, Guwahati, Assam, India

3Consultant, Department of Medicine, Downtown Hospital, Guwahati, Assam, India

*Corresponding e-mail: dr.lalitmohan7@gmail.com

Online published on 19 November, 2018.

Abstract

Sickle beta plus thalassemia (Hb S/β+ Th) is a rare inherited disorder among haemoglobinopathies. This disorder is inherited in an autosomal recessive manner. Sickle beta plus thalassemia patient usually have chronic haemolytic anaemia and rarely can present as vaso-occlusive painful crisis. Abdominal pain is frequently seen in vaso-occlusive painful crisis and may masquerade diseases such as acute appendicitis and cholecystitis. Acute pancreatitis is rarely included as a cause of abdominal pain in these patients. There are no systematic literature available which can give insight about this complication and its management. Here we report a case of sickle beta plus thalassemia presenting as acute pancreatitis.

Keywords

Sickle beta plus thalassemia, Acute pancreatitis, Haemoglobinopathies