Amelogenesis Imperfecta: A case report

Amelogenesis Imperfecta(AI) represents structural developmental defect of tooth enamel having complex inheritance pattern. It represents a group of heterogenous conditions. AI has several names such as hereditary enamel dysplasia, hereditary brown enamel, hereditary brown opalescent teeth. In this disorder, the enamel is hypoplastic, hypomineralized or both. It may show autosomal dominant, autosomal recessive, sex-linked or sporadic pattern. Here, we report three cases among six children of the same family with Amologenesis imperfecta, analyse the clinical presentation, diagnostic features and clinical complications of Amelogenesis imperfecta.