Multidisciplinary management of oligodontia polycystic ovarian syndrome: A rare case report

Oligodontia characterized by agenesis of more than six permanent teeth excluding third molars, is commonly associated with syndromes and rarely presents itself as an independent entity. Although its association with various syndromes has been studied extensively with great interest, its association with polycystic ovary syndrome (PCOS) has been rarely documented. PCOS is a condition manifested by pubertal hirsutism, menstrual irregularities and enlarged cystic ovaries. This case report presents multidisciplinary management of a case of oligodontia & PCOS with agenesis of twenty three permanent teeth. Oligodontia with PCOS is an extremely rare entity and has been presented only once in literature review. As oligodontia, PCOS has also shown genetic predisposition and several genes such as CYp11A, insulin gene, and follistatin gene have been identified but none has proven linkage to conclusive significant evidence. This occurrence of oligodontia with PCOS postulates a theory of genetic association which needs to be researched.