Hypohidrotic Ectodermal Dysplasia in a Young Male Patient

Ectodermal dysplasia represents a heterogenous group of disorders in which ectodermal derivatives are affected. It is an X-linked recessive condition hence females are commonly affected by this condition. There is aberrant morphogenesis of skin and embryonic ectodermal structures of the oral cavity. Generally, it is manifested by a triad of hypodontia, hypohydrosis and hypotrichosis. These patients have lustrous, thin and dry skin, fine and scanty kinky hair. Intra-orally partial anodontia, with an underdeveloped alveolar process is seen. We present a rare case of ectodermal dysplasia in a 17-year-old male patient with only a single tooth for documentation.