Late Onset Nevus of Ota - A Rare Presentation

Nevus of Ota, blue hyperpigmentation along the first and second branches of trigeminal nerve involves face, forehead, eyebrows, nose and eye (especially sclera). Late onset adulthood presentation, a rare presentation, represents stimulation by amelanotic melanocytes by potent stimuli like female sex hormones, trauma, infection. This condition in late onset, warrants detail investigations to rule out other associated autoimmune disorders and malignant change of nevus. This case highlights the importance of recognizing this entity even when the onset is late.