Primary Angiosarcoma of spleen-A rare case report from rural hospital

Primary angiosarcoma of the spleen is a very rare malignant neoplasm. It comprises less than 1% of all splenic sarcomas. It may present with non-traumatic spontaneous rupture of the spleen and lethal hemorrhage. It is difficult to diagnose clinically and has a variable morphological spectrum. It is a highly aggressive malignant tumor having poor prognosis. It is usually found in adults above 40 years of age. A 22 year old female presented with abdominal pain and mass of four month duration. Physical examination revealed splenomegaly and diffuse tenderness all over the abdomen. Following computed tomography scan a possible clinical diagnosis of giant cavernous hamangioma of the spleen was made. Histopathology following splenectomy revealed angiosarcoma. We report this rare case along with review of literature.