Myxoid Neurothekeoma: Report of a rare tumour at unusual site

Neurothekeoma is a rare benign soft tissue tumor of uncertain histogenesis which affects adolescents and young adults. It is rare to find these tumors occurring in children. Neurothekeoma usually presents with a small, solitary, and slow-growing nodule or papule on the upper body.

We describe a case of a 9-year-old girl having large (5x4x1) painful swelling over back of 2 months duration. After total resection of the tumor, histological examination and immunostaining confirmed the diagnosis of myxoid neurothekeoma. The clinicopathological features of this rare tumor and its important differential diagnoses are discussed.

Neurothekeoma is a rare tumour in children and its’ myxoid variant is even rarer. This benign tumour has to be differentiated from other malignant tumors as it has good prognosis.