Dentinogenesis Imperfecta Associated with Osteogenesis Imperfecta Type I

Dentinogenesis imperfecta(DI) belongs to a group of genetically conditioned dentin dysplasia and is characterized clinically by an opalescent amber appearance of the dentin. The teeth with DI show a grayish-blue to brown hue with dislodged enamel, dysplastic dentine with irregulardentinal tubules and interglobular dentine, short roots and pulpal obliteration, which all may lead to rapid and extensive attrition. DI can appear as a separate disorder or with osteogenesisimperfecta(OI). Osteogenesisimperfecta(OI) comprises a heterogeneous group of disorders characterized by bone fragility, frequent fractures, and low bone mass. A case of DI associated with OI are presented in this paper with a purpose to present the dental and skeletal characteristics of DI associated with OI in mild form.