Ameloblastic carcinoma of the mandible: A rare entity

Ameloblastic carcinoma (AC) is a very rare malignant odontogenic epithelial tumor of the jaws that has histological features of both ameloblastoma and carcinoma. It occurs primarily in the mandible in a wide range of age groups without any gender predilection. The clinical presentation of AC is variable; it may present as a cystic lesion with benign clinical features or as an aggressive tissue mass with extensive local destruction. Surgical En Bloc excision is the treatment of choice. Radiotherapy and chemotherapy seem to be of limited value for the treatment of AC. Long-term follow-up with periodic reassessment is mandatory. We are presenting a case report of AC in a very young patient, with literature review.