Journal of Oral Sign
  • Year: 2011
  • Volume: 3
  • Issue: 3

Cleidocranial Dysplasia - a case report

  • Author:
  • Nitin Agarwal1,, Saurabh Mathur2, Kirti Agarwal3, Mariam Khan4
  • Total Page Count: 4
  • Page Number: 164 to 167

1Department Of Oral Medicine and Radiology, Sardar Patel Post Graduate Institute of Dental and Medical Sciences, Lucknow, Uttar Pradesh, India

2Department Of Oral Medicine and Radiology, Saraswati Dental College, Lucknow, Uttar Pradesh, India

3Department Of Pedodontics, Saraswati Dental College, Lucknow, Uttar Pradesh, India

4Department Of Oral Medicine and Radiology, Saraswati Dental College, Lucknow, Uttar Pradesh, India

*Correspondance Dr. Nitin Agarwal, Professor, Department of Oral Medicine & Radiology, Sardar Patel Post Graduate Institute of Dental and Medical Sciences, RaeBariely Road, Lucknow, U.P. nitinmds@yahoo.com; Mobile No:9335206034

Online published on 12 June, 2012.

Abstract

Cleidocranial Dysplasia (CCD) is a rare congenital disorder of bone inherited as an autosomal dominant genetic trait. Cleidocranial Dysplasia previously known as Cleidocranial Dysostosis is characterized by abnormalities of skull, teeth, jaws and shoulder girdle as well as occasional stunting of the long bones. The principle oral manifestations are delayed exfoliation of primary teeth with multiple impacted permanent and supernumerary teeth. Hereby we present a case report of an 18 -year old male patient because of its rarity and the classical features of cleidocranial dysplasia.

Keywords

Cleidocranial dysplasia, Cleidocranial Dysostosis, Autosomal dominant, Ocular hypertelorism, Hypoplasia of clavicles