A Fatal Traumatic Outcome by Trivial Injury in A Haemophilia Case: A Rare Case Report

Haemophilia is a clinical syndrome affecting males usually and characterized by inherited tendency to bleed excessively following slight injury. Haemophilia is caused by a specific defect of coagulation factor VIII. The main concern associated with the disease is bleeding, especially after trauma and surgeries. The most serious site of bleeding for patients with haemophilia is the central nervous system. We reported a case of a 20 year-old person with a past medical history of haemophilia who came to the emergency department, SMS hospital, Jaipur with presenting complain of severe headache. Patient died after few days due to intracranial hemorrhage despite intensive treatment. Medico-legal autopsy was conducted on the same day. On autopsy brain was oedematous with tense duramater with underlying massive haemorrhagic blood clot. Intracranial hemorrhage (ICH) in patients with haemophilia can occur spontaneously or following mild head trauma however no guidelines exist for this approach. Most dramatic manifestation of Haemophilia is exsanguinating hemorrhage from a trivial traumatic injury. The most important aspect of ICH management is the early replacement therapy of deficient coagulation factors in haemophilic patients after every head trauma, even when considered minor. This prompt treatment will increase the chances of a better prognosis in haemophilic patients..