Medico-Legal Update
  • Year: 2017
  • Volume: 17
  • Issue: 1

Giant Malignant Peripheral Nerve Sheath Tumor with Intraspinal & Extraspinal Extension-A Rare Entity

1Associate Professor, Pathology, Mahatma Gandhi Medical College, Jaipur, Rajasthan

2Professor & Head of the, Department Neurosurgery, Mahatma Gandhi Medical College, Jaipur, Rajasthan

3Professor & Unit Head, General Surgery, Mahatma Gandhi Medical College, Jaipur, Rajasthan

4Assistant Professor, Neurosurgery, Mahatma Gandhi Medical College, Jaipur, Rajasthan

*Corresponding author: Dr. Surabhi Tyagi Associate Professor, Pathology, Mahatma Gandhi Medical College, Jaipur, Rajasthan, Mobile-09602779752 Email = dr_tyagi_surabhi@yahoo.co.in

Online published on 7 February, 2017.

Abstract

Malignant peripheral nerve sheath tumors are a rare variety of soft tissue sarcomas of ectomesenchymal origin. They originate from peripheral nerves or from cells associated with the nerve sheath such as schwann cells, perineural cells or fibroblasts. Due to their origin from many cell types, the presentation varies from case to case. They cause spinal cord compression with secondary changes in the surrounding bone and extension of tumor mass in the paraspinal and reterospinal region to a variable extent.

We present a case of giant MPNST with intraspinal component and extension to paraspinal and reterospinal region.

Keywords

MPNST, intraspinal, extraspinal, paraspinal, retrospinal